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214-456-6040
Fax: 214-456-6320
Plano
469-497-2501
Fax: 469-497-2507
Park Cities
469-488-7000
Fax: 469-488-7001
Prosper
469-303-5000
Fax: 214-867-9511
Our experienced pediatric surgeons are skilled in surgical procedures to treat Hirschsprung disease, a disorder that affects nerve cells in a child’s intestine. At the Colorectal and Pelvic Center at Children's Health℠, our multispecialty team diagnoses and treats Hirschsprung disease and other complex conditions of the digestive system. We bring together our expertise from several medical fields to provide compassionate care to improve your child’s health, well-being and quality of life.
214-456-6040
Fax: 214-456-6320
469-497-2501
Fax: 469-497-2507
469-488-7000
Fax: 469-488-7001
469-303-5000
Fax: 214-867-9511
Children who are born with Hirschsprung disease are missing certain nerve cells in the intestine, most commonly the large intestine. The condition affects the coordinated squeezing action called peristalsis, which moves stool (poop) through the intestines. Hirschsprung disease slows or stops stool from moving through, and the intestine becomes blocked.
To help your child have normal bowel movements, our surgeons perform a minimally invasive procedure. Surgeons first remove the section of the intestine that is missing nerve cells. They connect the healthy section to the anus (end of the large intestine where stool exits the body). In many cases, our surgeons perform this procedure in a single operation.
The key benefit of the laparoscopic pull-through procedure is that it removes the section of intestine with missing nerve cells to remove the blockage. After the procedure, the child will have bowel movements more easily as stool moves more normally through the intestines and out of the body through the anus.
The laparoscopic pull-through is a minimally invasive procedure that requires a few tiny incisions (cuts) on the abdomen (belly) to access the treatment area. In some cases, we may perform this procedure through the anus (transanal approach), which requires no incisions on the abdomen.
Benefits of our minimally invasive approaches include:
Your child’s care team works carefully to minimize any risks of complications with a laparoscopic pull-through procedure. Our surgeons and their teams have years of experience performing this procedure on infants and young children, which reduces the risk of potential complications. If a problem occurs, we quickly take steps to protect your child’s health. Your child’s care team will discuss possible risks of a laparoscopic pull-through surgery with you before the procedure.
In general, risks may include:
After pull-through surgery, children with Hirschsprung’s disease can still develop enterocolitis, an infection in the large intestine. Learn more about Hirschsprung’s disease and how we manage related issues such as enterocolitis.
Your child may need one or more surgeries over several months to fully repair the large intestine, depending on how much of the intestine is affected by Hirschsprung disease. The disease may affect only the rectum (lower end of the large intestine), a large section of the large intestine, the entire large intestine or, in very rare cases, part or all of the small intestine.
At the Colorectal and Pelvic Center, our surgeons have the expertise to treat all types of Hirschsprung disease, whether it affects a short segment or the entire small and large intestine. Whenever possible, we perform a single-stage operation to reconstruct the intestine. We work closely with you and your family to help you understand your child’s specific needs and decide on the right treatment options for them.
If needed, your child may have an ostomy as the first stage of treatment. In this procedure, the surgeon creates an opening in the belly and connects the intestine to it. Your child will have a collection bag attached to the opening to collect stool as it leaves the body.
With an ostomy, your child can eat and digest normally, and they will continue to grow before the laparoscopic pull-through procedure.
Often, our surgeons can perform this procedure shortly after birth, when we first diagnose Hirschsprung disease, so your child may not need an ostomy. First, our surgeons take one or more tissue samples (biopsy) of your child's intestines to identify the areas that lack nerve cells.
The surgeons then remove the diseased sections of intestine using a scope (narrow camera) and surgical instruments inserted through small incisions. When possible, we perform the pull-through procedure entirely through the child's anus, which requires no incisions and leaves no scars.
We then attach the end of the remaining, healthy intestine to the child's anus to construct a fully functioning large intestine (and part of the small intestine, if needed). By removing the part where nerve cells are missing, we ensure that the remaining large intestine has working nerve cells for proper bowel function.
If your child had an ostomy as the first stage of surgery, our surgeons sometimes close it during the pull-through procedure. In other cases, we close the ostomy in a separate procedure several weeks after the pull-through procedure, once the anal area has healed.
Most children need to stay in the hospital for a few days after a laparoscopic pull-through procedure for Hirschsprung disease. Before you leave the hospital, your child’s care team will provide you with complete instructions for how to care for your child at home.
Because your child will likely pass several stools a day at first, the skin around their anus may become irritated (severe diaper rash). We will teach you how to care for the skin in that area and how to keep any abdominal incisions clean and dry.
As you decide on treatment options for your child, you may want to ask the care team questions such as:
Our multispecialty team works together to help children overcome even the most complex types of Hirschsprung disease and other digestive disorders. We’ll stay by your side, every step of the way, to provide the care your child needs to achieve their best health.
Most children heal well from the procedure without complications. At first, your child may have frequent, loose stools, so it’s important to take good care of their skin to help prevent severe diaper rash.
An intestinal infection, Hirschsprung-associated enterocolitis (HAEC), can occur even after surgery. Although HAEC usually stops as a child gets older, it can become life-threatening.
We can quickly treat HAEC with antibiotics, so please contact us immediately if your child experiences symptoms such as:
For toilet training your child, you can start at the usual age, when they are age 2 to 3. A child who has Hirschsprung disease may take longer to control their bowel movements. At our Colorectal and Pelvic Center, we offer a comprehensive bowel management program to help your child achieve bowel control and avoid constipation or stool accidents. We work closely with you and your child to customize a program specifically for their unique needs.
Children usually don’t need to follow a special diet after surgery for Hirschsprung disease. Some types of Hirschsprung disease affect a child’s entire large intestine and part of the small intestine. After surgery to remove the affected parts of the intestines, a child may have problems getting enough nutrients and may need nutritional support or other treatments. Our care team can connect you with registered dietitians at Children’s Health for nutritional planning.
Children born with Hirschsprung disease need ongoing follow-up care. Some children may experience severe constipation and bowel incontinence, which, if not treated promptly, can lead to more serious conditions. Your child may need additional surgeries later in life to treat these issues. It’s important to continue to bring them to the Colorectal and Pelvic Center for follow-up care, where we can adjust their care plan as needed.
Some children may develop issues with body self-image and may benefit from psychological support. Our center offers access to pediatric psychologists, Child Life specialists and social workers for therapy and other services. Being proactive can empower young adults to take a larger role in managing their own condition, which can result in lifelong health benefits.
As your child becomes an adult, their health needs change. We can help your child transition to an adult care provider with experience in treating adults with Hirschsprung disease. Some adults who received care for this condition as children may experience continuing bowel issues. That’s why it’s critical that they receive ongoing care throughout their lives.